Abstract
P 059
Orbital chondromyxoid fibroma
Ludwig M. Heindl1, Kerstin U. Amann2, Arndt Hartmann2, Friedrich E. Kruse1, Leonard Holbach1
1Augenklinik mit Poliklinik, Universität Erlangen-Nürnberg, Erlangen, 2Institut für Pathologie, Universität Erlangen-Nürnberg, Erlangen
Background
Primary tumors of orbital bone are rare constituting up to 2% of all orbital masses. Chondromyxoid fibroma is one of the least common tumors of bone, comprising less than 1% of bone tumors and less than 2% of benign bone tumors. Orbital chondromyxoid fibroma has not been clearly documented in the ophthalmic literature. Herein, we report for the first time the clinicopathologic features of an orbital chondromyxoid fibroma arising from the frontal bone.
Method
Single interventional case report presenting clinical, imaging, histopathologic, immunohisto-chemical and ultrastructural findings.
Results
A 37-year-old female presented with slowly progressive swelling of the left upper eyelid temporally associated with occasional headache and shooting pain for three years. On examination, the left eye showed 4 mm of proptosis with downward displacement, mild blepharoptosis and choroidal folds at the posterior pole. CT disclosed a superotemporal, noninfiltrative orbital mass with erosion of the adjacent frontal bone. The patient underwent transcutaneous extraperiosteal orbitotomy with en bloc resection including tumor, surrounding periosteum and adjacent bony wall. Histopathologic, immunohistochemical and ultrastructural findings revealed a chondromyxoid fibroma. Two years after surgery no evidence of local recurrence or metastatic disease can be detected.
Conclusion
Chondromyxoid fibroma should be considered as a rare benign lesion in the differential diagnosis of primary orbital bone tumors.
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