Abstract

P 165

Complete visual restoration after the implantation of an aniridia lens in bilateral congenital aniridia

Georgia Milioti1, Nikolaos Kozeis2, Zisis Gkatzioufas3, Ursula Löw3, Kouris Ninios3, Berthold Seitz3
1Klinik für Augenheilkunde, Klinikum Saarbrücken; 2Augenklinik, Hippokrateion Allgemeinkrankenhaus, Thessaloniki, Greece; 3Klinik für Augenheilkunde, Universitätskliniken des Saarlandes, Homburg/Saar

Objective
Aniridia is a congenital, hereditary, bilateral extreme form of iris hypoplasia. The congenital aniridia leads to very early eye development arrest, and when the baby is born, most of the eye is underdeveloped to some degree. However, the clinical manifestations of aniridia varies considerably.
Methods
A 35-years-old lady with bilateral congenital aniridia of sporadic type was complaining of gradual reduction of her visual acuity and increasing photophobia during the last months. During the ocular examination we found that the best corrected visual acuity was 0.2 in the right eye and 0.3 in the left eye. The patient had complete aniridia and she started developing a corticalis cataract in both eyes. The cataract operation was performed as a phacoemulsification with an aniridia intraocular lens (from Morcher). One month after surgery, visual acuity increased to 0.8 in both eyes. The photophobia was markedly reduced.
Conclusions
In our patient an almost complete visual restoration after cataract extraction and implantation of an intraocular aniridia lens occured in both eyes. We suspect that the development of a cataract in childhood has led to the formation of an “artificial pupil” and this may have prevented  a deeper amblyopia.

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